Which disease is the most common inherited juvenile macular degeneration?

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The main concept is identifying the most common inherited macular degeneration that begins in youth. Stargardt disease fits this best. It typically presents in adolescence or early adulthood with painless central vision loss, while peripheral vision is often preserved early on. It is usually due to mutations in the ABCA4 gene and inherited in an autosomal recessive pattern, leading to accumulation of lipofuscin in the retinal pigment epithelium and characteristic macular flecks. This combination of early central vision loss and the genetic, juvenile-onset macular pattern makes Stargardt disease the most common inherited juvenile macular degeneration. By contrast, Leber congenital amaurosis is seen from birth, retinitis pigmentosa starts with night blindness and peripheral loss, and Best disease is a different vitelliform macular dystrophy with its own inheritance pattern, not the most common juvenile macular issue.